產(chǎn)品詳情
簡單介紹：
Anti-ATXN3L抗體產(chǎn)品質量穩(wěn)定，實驗效果明顯，貨期快，價格優(yōu)惠，歡迎垂詢訂購！我公司長期供應**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關試劑、熒光標記抗體、單克隆抗體、多克隆抗體、各種標記的二抗IgG/IgM/IgD/IgA等科研實驗抗體。Anti-ATXN3L抗體用于**組化實驗,WB實驗,相應的標記抗體有HRP標記抗體,FITC標記,BIO等。
詳情介紹：
Rabbit Anti-ATXN3L
Cat. Number:
Anti-ATXN3L抗體KL-4807R
Quantity size:
0.2ml
Concentration:
1mg/ml Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
Defects in ATXN3 Anti-ATXN3L抗體are the cause of spinocerebellar ataxia type 3 (SCA3) ; also known as Machado-Joseph disease (MJD). Spinocerebellar ataxia is a clinically and genetically heterogeneous group of cerebellar disorders. Patients show progressive incoordination of gait and often poor coordination of hands, speech and eye movements, due to degeneration of the cerebellum with variable involvement of the brainstem and spinal cord. SCA3 belongs to the autosomal dominant cerebellar ataxias type I (ADCA I) which are characterized by cerebellar ataxia in combination with additional clinical features like optic atrophy, ophthalmoplegia, bulbar and extrapyramidal signs, peripheral neuropathy and dementia. The molecular defect in SCA3 is the a CAG repeat expansion in ATXN3 coding region. Longer expansions result in earlier onset and more severe clinical manifestations of the disease.
Also known as:
ATX3L_HUMAN; Anti-ATXN3L抗體ATXN3L; Machado-Joseph disease protein 1-like; MJDL; Putative ataxin-3-like protein.
Specificity:
●
Rabbit Polyclonal IgG, affinity purified by Protein A.
●
Reacts with: Human, .
●
Immunogen: KLH conjugated synthetic peptide derived from human ATXN3L.
●
Predicted Molecular Weight: 41kDa.
Storage:
Shipped at 4℃, Anti-ATXN3L抗體Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500 IHC-P=1:100-500 IHC-F=1:100-500 IF=1:50-200
Not yet tested in other applications.
Optimal working Anti-ATXN3L抗體dilutions must be determined by the end user.
Not yet tested in other applications.
Optimal working Anti-ATXN3L抗體dilutions must be determined by the end user.
kl153Po01 甲胎蛋白(αFP)多克隆抗體 Polyclonal Antibody to Alpha-Fetoprotein (aFP)
kl153Bo01 甲胎蛋白(αFP)多克隆抗體 Polyclonal Antibody to Alpha-Fetoprotein (aFP)
kl153Ga01 甲胎蛋白(αFP)多克隆抗體 Polyclonal Antibody to Alpha-Fetoprotein (aFP)
kl153Eq01 甲胎蛋白(αFP)多克隆抗體 Polyclonal Antibody to Alpha-Fetoprotein (aFP)
kl084Ge01 胰安肽(Aglycin)多克隆抗體 Polyclonal Antibody to Aglycin
kl028Mu01 白蛋白(ALB)多克隆抗體 Polyclonal Antibody to Albumin (ALB)
kl028Ra01 白蛋白(ALB)多克隆抗體 Polyclonal Antibody to Albumin (ALB)
kl028Gu01 白蛋白(ALB)多克隆抗體 Polyclonal Antibody to Albumin (ALB)
kl028Rb52 白蛋白(ALB)多克隆抗體 Polyclonal Antibody to Albumin (ALB)
kl028Po01 白蛋白(ALB)多克隆抗體 Polyclonal Antibody to Albumin (ALB)
kl028Cp01 白蛋白(ALB)多克隆抗體 Polyclonal Antibody to Albumin (ALB)
kl028Eq01 白蛋白(ALB)多克隆抗體 Polyclonal Antibody to Albumin (ALB)
kl028An01 白蛋白(ALB)多克隆抗體 Polyclonal Antibody to Albumin (ALB)
kl028Ha01 白蛋白(ALB)多克隆抗體 Polyclonal Antibody to Albumin (ALB)
kl816Po01 α1-酸性糖蛋白(α1AGP)多克隆抗體 Polyclonal Antibody to Alpha-1-Acid Glycoprotein (a1AGP)
kl816Bo01 α1-酸性糖蛋白(α1AGP)多克隆抗體 Polyclonal Antibody to Alpha-1-Acid Glycoprotein (a1AGP)
kl697Rb51 α1-抗胰蛋白酶(α1AT)多克隆抗體 Polyclonal Antibody to Alpha-1-Antitrypsin (a1AT)
kl697Po01 α1-抗胰蛋白酶(α1AT)多克隆抗體 Polyclonal Antibody to Alpha-1-Antitrypsin (a1AT)
